ABSTRACT
The biliary cystadenocarcinomas are very rare malignant tumor. The etiology is unclear, this tumor may be develop from malignant transformation of begin cystadenoma. The tumor appears typically as a cystic mass which contains papillary projections or internal septations. Papillary projections are seen on the inner surface of the cyst which present numerous papillary protrusion typical to this rare tumor. Excessive mucin secretion produced by the tumor cells and its retention in the common bile duct may cause bile stasis leading to obstructive jaundice. Common presenting symptoms are abdominal fullness, pain, nausea, palpable mass and asymptomatic. The available diagnostic tools are CT and sonography, but histologic examination can be made diagnostic confirm. Surgical resection yields excellent results. We were experienced a cystadecarcinoma with early gallbladder cancer, then report with reference.